Embryonal Rhabdomyosarcoma of The Forearm: A Diagnostic Dilemma and Surgical Management
Daftar Isi:
- Establishing the diagnosis of primary soft-tissue sarcoma is a difficult task even for an experienced clinician. There is a plethora of clinical manifestation yet its radiological appearancecan be very deceiving in every way. We report a case of embryonal rhabdomyosarcoma in an adultfemale with lump in her left distal forearm, with clinical manifestation and radiological appearance thatimmitate bone sarcoma. The diagnosis was not established until the biopsy result came up whichalso confirmed by immunohistochemistry stain. The treatment is a novelty limb salvage surgery withmodified forearm segmental amputation and shortening procedure. Six months after the surgery thepatient had good functional outcome without local recurrence and distant metastasis. Keywords: embryonal rhabdomyosarcoma, limb salvage surgery, forearm segmental amputation Rabdomiosarkoma Embrional Antebrakhii:suatu Masalah Diagnosis dan Penatalaksanaan Bedah Abstrak Menegakkan diagnosis sarkoma jaringan lunak primer merupakan pekerjaan sulit, bahkan di tangan klinisi yang berpengalaman sekalipun. Sejumlah kasus sarkoma jaringan lunak menunjukkan manifestasi klinis, tetapi gambaran radiologisnya tidak sesuai. Pada makalah ini dilaporkan satu kasus rabdomiosarkoma embrional pada perempuan dewasa dengan benjolan di antebrachii distalkiri dengan manifestasi klinis dan gambaran radiologi menyerupai sarkoma tulang. Diagnosis pastiditegakkan setelah pemeriksaan pulasan imunohistokimia. Penatalaksanaan bedah yang dilakukanmerupakan inovasi baru dengan cara limb salvage surgery amputasi segmental antebrachii yangdimodifikasi dan shorthening procedure. Pada pengamatan 6 bulan pascabedah, pasien memilikiluaran fungsional yang baik tanpa disertai rekurensi lokal dan metastasis jauh. Kata kunci: rabdomiosarkoma embrional, limb salvage surgery, amputasi antebrakhii segmental