PERAWATAN GIGI PADA ANAK DENGAN MAPLE SYRUP URINE DISEASE (LAPORAN KASUS)

Main Authors: Fajari, Tri; Pedodontics Residency Program, Faculty of Dentistry, Universitas Indonesia, Jakarta 10430, Suwelo, Ismu Suharsono; Department of Pedodontics, Faculty of Dentistry, Universitas Indonesia, Jakarta 10430
Format: Article info application/pdf eJournal
Bahasa: eng
Terbitan: Faculty of Dentistry, University of Indonesia , 2015
Subjects:
Online Access: http://www.jdentistry.ui.ac.id/index.php/JDI/article/view/389
http://www.jdentistry.ui.ac.id/index.php/JDI/article/view/389/287
Daftar Isi:
  • Maple Syrup Urine Disease is a disparity of leusin decarboxilation, and isoleusin of valin defect that is synthesized with complex enzyme systems. It is a rare disease and represents disparity. In some cases can generate ketosis that grows according to health change and can cause comma. Dental treatment of a child with Maple Syrup Urine Disease was not clearly mentioned, there is only a factor such as infection, which is very dangerous at any age, and can generate irregular metabolism. Dental treatment of a child with Maple Syrup Urine Disease accompanied by mental retardation must be done continuously to avoid infection that can result in the death of the patients.