Scleroderma Patients with Pulmonary Artery Hypertension: A Case Report
| Main Authors: | Muhammad Miftahussurur, Joewono Soeroso |
|---|---|
| Format: | BookSection PeerReviewed Book |
| Bahasa: | eng |
| Terbitan: |
SCITEPREES-Science and Technology Publications, Lda
, 2017
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| Subjects: | |
| Online Access: |
http://repository.unair.ac.id/91963/1/3p.%20Scleroderma%20Patients%20with%20Pulmonary%20Artery%20Hypertension_%20A%20Case%20Report.pdf http://repository.unair.ac.id/91963/2/3.%20scleroderma%20patient.pdf http://repository.unair.ac.id/91963/5/scleroderma.pdf http://repository.unair.ac.id/91963/ https://www.scitepress.org/PublicationsDetail.aspx?ID=0NSueRAnMDE=&t=1 |
Daftar Isi:
- Scleroderma or systemic sclerosis (SSc) is a multiorgan connective tissue disorder involving the skin, lungs, heart, digestive tract, musculoskeletal system, and peripheral circulation. Pulmonary arterial hypertension (PAH) is an increase in mean pulmonary artery pressure > 25 mmHg as measured by echocardiography or catheterization. The incidence of PAHs with SSc is so rare that reports, in this case, are necessary. Objective: to describe the management of PAH patients with SSc. Case: a 32-year-old patient experiencing PAHs with SSc has stiffness of the mouth and is difficult to open. The ECG shows a sinus tachycardia with a Right axis destination and a cardiomegaly thorax photo with a 64% cardio-thorax ratio. Some clinical data show autoimmunity. Treatment is oxygen, diuretic, thrombolytic, and immunosuppressive drugs. Conclusions: Reports of PAH treatment with SSC are essential for the improvement of therapy