Surgical outcome of scoliosis in Marfan syndrome: a case series report
| Main Author: | Komang Agung Irianto Suryaningrat, NIDN. 8819130017 |
|---|---|
| Format: | Article PeerReviewed Book |
| Bahasa: | ind |
| Terbitan: |
Fakultas Kedokteran Universitas Gadjah Mada
, 2018
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| Subjects: | |
| Online Access: |
http://repository.unair.ac.id/85268/1/Peer%20Surgical%20outcome.pdf http://repository.unair.ac.id/85268/2/Dr%20Komang%20Berkala%20Ilmu%20Kedokteran%20UGM%202018.pdf http://repository.unair.ac.id/85268/6/Surgical%20outcome%20of%20scoliosis%20in%20Marfan%20syndrome.pdf http://repository.unair.ac.id/85268/ https://jurnal.ugm.ac.id/bik/article/view/15621 |
Daftar Isi:
- Scoliosis in marfan syndrome (MFS) manifests on 60% patients. Moreover, the scoliosis noticeable in earlier age is more progressive, refracted, and rigid compared to idiopathic adult scoliosis. The surgical correction provides notorious higher perioperative risk, whereas conservative treatment using brace is not effective to prevent progressivity of the scoliosis. In this a case report, we reported the surgical outcome of MFS scoliais patients with MFS who operated using posterior fusion instrumentation by mean of the quality of life SF-36 questioner. This was a retrospective case series involving five MFS scoliosis patients who underwent posterior fusion instrumentation with initial Cobb angle of 87.417.57o and initial kyphotic angle of 32.8 ± 14.52o. Clinical, radiological and quality of life of the patients based on SF-36 questionnaire were evaluated within 6-36 months follow up. Post-operative showed the Cobb angle become 46.2 ± 16.3o and the kyphotic angle become 21.6 ± 9.94o. No intraoperative or post-operative complications were observed. After 6-36 months follow up, the Cobb angle became 45.2 ± 17.48o and the kyphotic angle became 21.6 ± 9.94o. In addition, all patients had physical and mental health scored similar to 2 years post surgery scoliosis scoring according to SF-36 orthopedic scoring guidelines. I conclusion, the surgical outcome of posterior fusion instrumentation in MFS scoliosis showed good correction of Cobb angle and Kyphotic angle. The quality of life of the patients based on physical and mental health questionnaire is satisfactory.