A Rare Case of Lymphangioleiomyomatosis in Sri Lanka
| Main Authors: | Dushantha Madegedara, Asela Rasika Bandara, Sachini Seneviratne, Samadara Nakandala, Rathnayake R.M.D.H.M |
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| Format: | Article eJournal |
| Bahasa: | eng |
| Terbitan: |
, 2018
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| Subjects: | |
| Online Access: |
https://zenodo.org/record/3540519 |
Daftar Isi:
- Lymphangioleiomyomatosis (LAM) is a rare disease, found approximately 1 in 1,000,000 in general population.LAM is characterized by progressive non-neoplastic proliferation of smooth muscle-like LAM cells resulting in destruction and cystic remodeling of lung parenchyma. Progressive dyspnoea, recurrent pneumothorax, chylothorax, cough, and hemoptysis are the usual manifestations of the disease. Demonstration of diffuse cysts in lung parenchyma in high resolution computered tomography (HRCT) with typical clinical features can diagnose lymphangioleiomyomatosis without histology, which is necessary for uncertain cases. LAM almost exclusively occurs females of reproductive age group. However rare cases of LAM have been reported in children and postmenopausal females and even in men. We describe a rare case of lymphangioleiomyomatosis in a postmenopausal Sri Lankan woman.